In rigid person syndrome, the individual has intense stiffness that can manifest throughout the body or only in the legs, for example, when they are affected the person can walk like a soldier because they cannot move their muscles and joints very well.
It is an autoimmune disease that usually develops between the ages of 40 and 50 years and is also known as Moersch-Woltmann syndrome, rigid man syndrome, only about 5% of cases occur in childhood or adolescence.
Rigid person’s disease syndrome can manifest in 6 different ways
Typically, the person with this syndrome not only has this disease, but also other autoimmune diseases such as type 1 diabetes, thyroid disease, or vitiligo, for example.
This disease can be cured with the treatment indicated by your doctor, but treatment can take time.
Symptoms of rigid person syndrome are severe and include
Because of these symptoms, the person may have hyperlordosis and pain in the spine, especially when the back muscles are affected and can fall frequently because they cannot move and balance properly.
Intense muscle stiffness usually occurs after a period of stress such as a new job or to do a job in public, and muscle stiffness does not occur during sleep and the deformities of the arms and legs are common due to the presence of these spasms, if left untreated.
Despite increased muscle tone in affected areas, tendon reflexes are normal, so diagnosis can be made with blood tests that look for specific antibodies and electromyography, as well as request x-rays, MRIs, and CT scans to rule out the possibility. other diseases.
Treatment of the rigid person should be performed with the use of drugs such as baclofen, spentronium, immunoglobulins, gabapentin and diazepam indicated by the neurologist, sometimes it may be necessary to remain in the intensive care unit to ensure the proper functioning of the lungs. heart during illness and duration of treatment can range from several weeks to several months.
Plasma transfusion and the use of monoclonal anti-CD20 antibodies (rituximab) may also be indicated and perform well. Most people diagnosed with this disease recover when they receive treatment.