Cimeter syndrome is a rare disease and is caused by the presence of a pulmonary vein, in the form of a Turkish sword called a scimitar, that drains the right lung into the vein in the lower cave instead of the left atrium.
The change in the shape of the vein results in changes in the size of the right lung, an increase in the contraction force of the heart, a deviation of the heart to the right side, a decrease in the right pulmonary artery, and abnormal blood flow. to the right lung.
- The severity of Scimitar syndrome varies from individual to individual.
- With patients who have the disease but show no signs or symptoms throughout their lives and others who have serious health problems.
- Such as pulmonary hypertension.
- Which can lead to death.
Symptoms of Scimitar syndrome may include
Diagnosis of cimitarra syndrome is done using tests such as chest x-rays, CT scans, and angiography to identify changes in the shape of the pulmonary artery.
Treatment of Scimitar syndrome consists of a surgical procedure that redirects the abnormal pulmonary vein from the lower vena cava to the left atrium of the heart, normalizing lung drainage.
Treatment should only be performed in cases of almost total blood diversion from the right pulmonary vein to the inferior vena cava or in cases of pulmonary hypertension.